What is glycogen?
Glycogen is the primary carbohydrate stored in the liver and muscle cells of animals. Glucose is stored inside the cells in the form of glycogen. The sugar needed for the body to provide energy for daily metabolic activities are provided by the glucose. And this glucose is converted into glycogen and also glycogen is catabolized back into glucose as per the times of requirement. There are a number of enzymes that accompany the process too.
So the process of converting glycogen back to glucose at times of immediate energy requirement to maintain the blood glucose levels is called glycogenolysis and the process of forming glycogen from glucose is called glycogenesis. Takes place when the blood glucose levels are sufficient or to allow the storage of excess glucose in liver and muscle cells.
What are glycogen storage disorders?
Glycogen storage disorders are formed due to the malfunctioning of a protein or enzymes (enzymes are made of proteins) responsible for glycogenolysis or gluconeogenesis. The enzyme disorders are the main reason why there will be an inadequate amount of glycogen produced in the body or the resultant effect like abnormal glycogen production.
If the enzymes linked with the glycogenolysis are affected it will lead to a low or excess levels of glucose in blood too. Resulting in conditions like hypoglycaemia (low levels of glucose in the body).
Different types of glycogen storage disorders.
Depending on which enzyme is lacking or functioning abnormally, there are mostly 12 types of glycogen storage disorders. The disorders likely affect the cells of the liver and muscles. It also tends to affect the kidney, heart, blood vessels, bowels, and the neural system also gradually. The important ten types being as follows,
- Von Gierke's disease (type I : most common)
- Pompe's disease (type II)
- Forbes-cori disease (type III)
- Andersen's disease (type IV)
- Mc ardle's disease (type V)
- Hers disease (type VI)
- Tarui's disease (type VII)
- Liver phosphorylase kinase deficiency (type IX)
- Fanconic- Bickel syndrome (type XI)
- Lewis disease (type 0)
How do you get glycogen disorders and what are the symptoms?
Mostly the glycogen disorders are inherited. Passed on through families via genes. The symptoms depend on the type of disorder.
- Type I, IV, VI, IX affects the liver.
- Type V, VII affects muscles.
- Type III affects both muscles and liver.
The common systems will include
In children
- Slow growth along with weak muscles.
- Low blood sugar levels leading to sweating, tremor, confusion, uncontrolled muscle movements and convulsions, drowsiness etc.
- Enlarged liver which doctors inspect on child's tummy.
- Obesity and kidney problems
- Bleeding disorders and clotting issues.
In case of teenagers and adults it can lead to fatigue and exhaustion even at the slightest of physical activities. Muscles can be weak and might even ace. Few disorders depending upon their underlying reasons can affect your immune system making you susceptible to infections.
Diagnosis and Treatment
Blood tests, biopsy and scanning are most adopted medical techniques to diagnose glycogen storage disorders. For treatment we need to stabilize that disarray in the glycogen and glucose levels of blood. Diet plan will help a lot. In Ayurveda a healthy diet and necessary physical activities corresponding to the health issues will heal your body to a greater extent. So stick to a diet plan. High protein content if given as an input and the use of nutritional supplements like glucose can be helpful.
Now the tricky cases appear as well, when the patients stop responding to nutritional supplements. In those instances we may occasionally go for liver transplant. For immunity to decrease, a regular antibiotic protection for the body to cope up against infection may also be adopted. Replacement therapy for enzymes are also administered now to reverse the condition ensuring their optimal functioning in metabolic reaction
So if you are searching for nutritional supplements, here are some of our best choices from Planet Ayurveda. Planet ayurveda is a trusted and famed organisation offering products across all over the world. The experts of planet ayurveda suggests some of the formulations for the management of these disorders which are as follows :-
- Kumar kalyan ras
- Energoplan syrup
- Arogyavardhini vati
- Nourish Maxx
- Ashwagandha Capsules
- Chanderprabha vati
Products Description
1. Kumar kalyan ras
It is a herbal mineral known to treat paediatric and heat related ailments with the help of their herbal formulations. The ingredients being kumari rasa (Aloe Vera juice extract), sheedha shuddha parada (purified mercury), abhraka basma (purified and processed mica) and a lot more ingredients blessed with therapeutic value. The herbal formulation is known for their ability to bring about the vitiated or decreased levels of pitta dosha back to their normalcy. It is to be consumed as 1 daily in chewable form.
Dosage- 1 tablet once a day with plain water after meals
2. Energoplan syrup
With the magical combination of herbs including amalaki ( Emblica officinalis), ashwagandha (withania somnifera), gokshura ( tribulus terrestris) and pippali ( piper longum) this syrup restores your energy level and maintain the active endurance power within the body. Planet ayurveda's energoplan syrup could be consumed daily by all family members. Its formulations will protect the body from harmful toxins and pillars the natural immune responses of the body.
Dosage- 2 tsp twice daily after meal
3. Arogyavardhini vati
This is an ayurvedic medicine in capsular form produced by planet Ayurveda to help fight against fever, skin and liver diseases. The formulations ate tridosha pacifiers making the body's optimal balance on vata, pita and kapha doshas within an endurable limit. It acts as an active digestive stimulant and improves bio-fire thereby keeping endotoxins in the body. The ingredients like haritaki (chebulic myrobalan fruit),amalaki (indian gooseberry), tranda and neem juice extracts help the same purpose.
Dosage - 2 tablets twice a day with plain water after meals
4. Chanderprabha vati
The 120 capsules tablets are more than enough for your nutritional requirements on a daily basis. It improves the overall functioning of the body. It brings back the disrupted kapha dosha levels back to normalcy as well as assists in the maintenance of optimal levels of vata. The ingredients like curuma longa (haridra), amala, guduchi(tinospora cordifolia) and pippali (piper nigrum) are known to weaken insulin resistance by 88% and enhance glucose uptake by the cells. Their weak anti-infective properties also come handy in conditions like glycogen storage disorders.
Dosage - 2 tablets twice a day with plain water after meals
5. Nourish Maxx
This is the pure vegan formula for nourishing the whole body. This can be your best choice of natural supplement to be coupled with a low fat diet and an active lifestyle. Prepared out of the herbal combinations containing shatavari ( Asparagus racemosus), safed musli ( Chlorophytum borivilianum), ashwagandha ( Withania somnifera) and gokshura (Tribulus terrestris). It is the plant based protein powder for better muscle strength to be consumed either in powder form or by boiling in water. This helps to improve tissue nutrition thereby providing strong and healthy movements and an effective motor activity system in the body.
Dosage- 1 tsp twice daily with plain water after meals
6. Ashwagandha Capsules
This is a renowned rejuvenative herb in Ayurveda widely used as an adaptogen for coping up with physiological as well as psychological stress. Ashwagandha pacifies Vata and Kapha because of its hot potency and unctuous nature. It is best known for supporting optimal anabolic reactions in the body. The same which we have incorporated in our capsules.
Dosage - 2 capsules twice daily with plain water after meals
Contact my assistant to provide you the costing / ordering and delivery information at - [email protected] or call at +91-172-5214030 Or Check Website - www.PlanetAyurveda.com
At last , we can conclude that the above-mentioned herbal formulations are very good and effective in managing Glycogen storage disorders.These formulations are free from any kind of preservative, chemical, additive and preservative and do not produce any adverse effects. For more queries you can consult online through [email protected].
