ABSTRACT
Hereditary motor sensory neuropathy commonly known as charcot marie tooth disease - is an inherited as well as progressive disorder. This condition is associated with the nervous system, the nervous system is the controlling center of the all body commands. It controls all the movements of the body and controls all processes of the body such as digestion, puberty, breathing and all other body processes. All the activities we perform, anything we feel, we say, all these are under the control of the nervous system. So if the nervous system is working properly then your whole body is healthy. But there are several conditions that are associated with the nervous system, among which one is HMSN disease, which is an inherited nervous disorder we are going to discuss in this article.
INTRODUCTION
Hereditary motor sensory neuropathy is an inherited nervous disorder that is also called as Charcot marie tooth disease. This disease is progressive in nature in which nerve cell deterioration is the main pathology. This concern is majorly seen in the legs and less commonly in the arms. The muscles of feet and hands get weak as the impulses towards these muscles are hampered. In addition to this there are a lot of symptoms to be faced that we will discuss further, so before studying the symptoms of HMSN let's discuss the causes of HMSN.
CAUSES
There is no certain cause of HMSN, this disease is inherited. Chromosomes 1 and 17 seem to be affected chromosomes with mutation. It is inherited in autosomal recessive, autosomal dominant and the x-linked manner. Beside this there are some risk factors of HMSN such as Americans worldwide and in the generations children are more affected.
SYMPTOMS
The symptoms of HMSN can vary from person to person and it's not possible to predict the age at which symptoms may appear. There are some early symptoms, main symptoms and later symptoms of HMSN, let's discuss further.
Early symptoms of HMSN
In the early stages it is difficult to mark symptoms, they are usually evaluated when it gets worsened. Following are some symptoms that are noticed in the early stages:
- Uncoordinated
- Face difficulty while walking as the affected one may face problems with raising their feet up from the ground.
- There is a kind of foot drop noticed, while lifting their feet the toes drops forward.
Main symptoms of HMSN
The main symptoms of HMSN are seen in the middle of 5-15 and the symptoms are not developed clearly until an affected one may lead to the middle or later ages. So below are the main symptoms of HMSN
- Weakness of muscles in the legs, feet and ankles.
- Feet are highly arched that leads to unstable ankle
- Hammer toes (curled toes)
- Lack of sensation in the feet and lesser than that in arms.
- Poor blood circulation leads to cold hands and feet.
- There is a wasting of muscles occurring in the lower legs that can lead to bottle shaped legs.
There are some additional symptoms that are noticed in some persons
- Tremor (uncontrolled shaking)
- Scoliosis (abnormal curvature of spine)
- Dysphagia (problem while swallowing)
- Difficulty while speaking
- Difficulty breathing
Later symptoms of HMSN
As the HMSN proceeds to the later stages the weakness in the muscles and the sensation loss get worsened that can start to affect the hands and arms the most. There is difficulty in performing even small tasks such as buttoning the shirt and performing day to day activities such as bathing, walking, sitting, etc. When they walk it puts strain on the muscles that further lead to joint and muscle pain. With growing age the mobility gets worse and a person may need an aid for walking.
DIAGNOSIS
The diagnosis of HMSN is done with the motor nerve conduction test and EMGs. A person to be diagnosed with HMSN should undergo a complete diagnostic and a clinical evaluation. The clinical diagnosis is done for the muscle weakness, atrophy and all types of sensory responses. For more clear diagnosis a blood DNA test is to be done.
AYURVEDIC VIEW OF HMSN
As we read earlier the HMSN is an inherited disorder, so as per ayurveda it is correlated with beeja dosha, which means the condition occurs with the defect in beejbhaga (sperm and ovum). Ashudh shukra and Ashudh artava (defected sperm and defected ovum) are considered as the main causes of this condition. If there is any defect in the gametes (sperm and ovum) of parents then the child should inherit the disease. Beeja dosha due to the fact that if the mother conceived when her uterus or artava (gamete) is not totally vitiated but troubled by imbalanced doshas because of her improper diet intake. If there is any defect due to beej bhaga then cause beeja dosha and the deformity will occur in the fetus. As it is an inherited disease, we may manage the symptoms of the disease and there are some natural herbs that manage the symptoms of the disease and make the affected person's life better by improving the quality of life.
HERBAL REMEDIES BY PLANET AYURVEDA FOR MANAGING HMSN
Planet Ayurveda is a GMP certified clinic which provides treatment for a wide range of diseases. All their remedies are formed under the guidance and supervision of M.D. ayurveda doctors and 100% purely vegetarian. Also while formulating their remedies they take care that any kind of added synthetic material should not be added to it like any sort of resins, fibre, colour, preservatives and all. For managing HMSN Planet Ayurveda listed 7 herbal remedies. Further we are going to discuss all about these herbal remedies and how it benefits the HMSN patients.
- ASHWAGANDHAGHAN VATI
- ATIRASADI CHURNA
- KUMARI SAAR
- TRIBULUS POWER
- MUSLI STRENGTH CAPSULES
- VRIHAT VATCHINTAMANI RAS
- NEUROGENIE CAPSULES
PRODUCT DESCRIPTION
1. ASHWAGANDHAGHAN VATI
Ashwagandhaghan vati by Planet Ayurveda is a herbal remedy in tablet form which consists of a single herb Ashwagandha (Withania somnifera). As we discussed earlier the HMSN is an inherited disease so we can focus on managing the symptoms of the person and making the day to day life more ebay. So mainly the vata dosha is responsible for maintaining the neurological symptoms. Ashwagandha ghan vati helps in balancing vata dosha this helps in maintaining the symptoms of the HMSN.
Dosage: 2 tablets twice daily after meals with plain water.
2. ATIRASADI CHURNA
Atirasadi churna is the herbal remedy in powder form prepared by Planet Ayurveda. It consists of various balya (strengthening) herbs such as safed musli (Chlorophytum borivilianum), kali musli (Curculigo orchioides), gokshura (tribulus terrestris), shatavari (Asparagus racemosus), ashwagandha (Withania somnifera) and various others. This herbal remedy boosts up the overall strength of the affected person and helps in preventing muscle wasting, muscle strain, pain in the muscles and nerves, etc. Thus makes it easier to perform day to day activities.
Dosage: 1 tsp twice daily after meals with warm milk.
3. KUMARI SAAR
Kumari saar is a herbal juice preparation formed by Planet Ayurveda with the help of juice extract of kumari (Aloe barbadensis) leaves. As we know the patients affected with HMSN need a perfect rejuvenation for leading a good quality life. This herbal remedy helps in providing that rejuvenating property to the patient and helps in boosting the immunity which makes the quality of life improved in the patient of HMSN.
Dosage: 2 tsp twice daily with plain water after meals.
4. TRIBULUS POWER
Tribulus power is a herbal remedy in capsule form that is formulated by Planet Ayurveda under the strict guidance of M.D. Ayurveda doctors. These capsules consist of pure herbal extract of gokshura (Tribulus terrestris) which contains various properties such as immunity-boosting and rejuvenating. So both these properties help in assisting the management of HMSN symptoms.
Dosage: 1 capsule twice daily with plain water after meals.
5. MUSLI STRENGTH CAPSULES
Musli strength capsules are available in capsules form and consist of standardized extracts of safed musli (Chlorophytum borivilianum) and gokshura (Tribulus terrestris). Safed musli is known for the rasayana (rejuvenates cells) and bruhmana (nourishing) properties. Gokshura consists of madhura rasa (sweet taste) which is also nourishing in nature. Both these herbs are very best in providing strength to the muscles and hence prevents the progressive muscle wasting in HMSN.
Dosage: 1 capsule twice daily with plain water after meals.
6. VRIHAT VATCHINTAMANI RAS
Vrihat vatchintamani ras is a classical ayurvedic formulation in tablet form. This is a herbo-mineral remedy which is prepared by Planet Ayurveda as per the method of preparation available in the classical texts. It consists of ingredients such as swarna bhasma (calyx of gold), rajat bhasma (calyx of silver), abhrak bhasma (calyx of mica) and various others. All the ingredients present in this ayurvedic formulation consists of miraculous vata balancing effects as the name suggests along with that it is balya in nature (strengthening) which provides strength to the muscles and nerves that alleviates the symptoms of HMSN.
Dosage: 1 tablet twice daily with plain water after meals.
7. NEUROGENIE CAPSULES
Neurogenie capsules by Planet Ayurveda consist of the standardized extract of Brahmi (Bacopa monnieri) and Ashwagandha (Withania somnifera). Brahmi (Bacopa monnieri) consists of antioxidant properties that aids in preventing the degeneration of the nerve cells thus restricting the further progress of the disease HMSN. Ashwagandha (Withania somnifera) contains wonderful rejuvenating and strengthening properties that help in managing the symptoms of HMSN such as muscle pain, difficulty in breathing, difficulty in lack of sensation, difficulty while walking, etc.
Dosage: 1 capsule twice daily with plain water after meals.
Contact Planet Ayurveda to provide you the costing / ordering and delivery information at - [email protected] or call at +91-172-5214040 Or Check Website - www.PlanetAyurveda.com
CONCLUSION
HMSN is an inherited disorder that is also called as Charcot marie tooth disease which is progressive in nature that includes nerve cell deterioration as the main pathology. . It occurs by the mutation (change) in the Chromosomes 1 and 17. In general the condition occurs due to transfer of defective genes from both the parents. According to Ayurveda HMSN is correlated to beeja dosha, which means the condition occurs with the defect in beejbhaga (sperm and ovum). Progressive muscle wasting, Severe disability, Disturbed gait, Decreased stability, Frequent falls, Difficulty in climbing stairs, Difficulty in walking, in short a person is unable to perform day to day activities. So if you are facing these issues, you must choose ayurveda treatment. It will improve your quality of life and make you better to perform day to day activities. For this purpose Planet Ayurveda is there for you with a miraculous list of herbal remedies, then stop worrying and start taking Ayurvedic medicine to improve your day to day life.
